Delta‑Aminolevulinic Acid (ALA)

Overview and Clinical Significance

Delta-Aminolevulinic Acid (ALA) is a precursor in the heme biosynthesis pathway, playing a crucial role in red blood cell production and mitochondrial function. It is synthesized in the liver and converted into porphobilinogen (PBG), a key intermediate in heme formation.

Clinical Significance

  • Heme Synthesis & Anemia: ALA is essential for hemoglobin production, and disruptions in its metabolism can lead to anemia and porphyria.
  • Porphyrias & Neurological Effects: Accumulation of ALA is linked to acute hepatic porphyrias, causing neurological symptoms, abdominal pain, and autonomic dysfunction.
  • Toxicity & Environmental Exposure: Elevated ALA levels may indicate lead poisoning, as lead inhibits enzymes in the heme pathway.
  • Kidney Function & Metabolism: ALA levels are monitored in renal disease, as impaired clearance can lead to accumulation.

ALA is a key biomarker in porphyria diagnostics, toxicology assessments, and metabolic health evaluations.

Increasing +

Decreasing -

Lead Poisoning

  • Mechanism:
    Lead exposure inhibits ALA dehydratase, causing ALA to accumulate.
  • Diagnostic Clue:
    Elevated ALA is a classic laboratory finding in lead poisoning and can help confirm toxic exposure.

Porphyrias

  • Association:
    Some forms of porphyria, disorders of heme synthesis, are associated with increased ALA levels.

Metabolic and Environmental Exposures

  • Enzyme Impairment:
    Certain chemicals or drugs may impair enzyme function in the heme pathway, leading to raised ALA levels.

Life-Stage Considerations

  • Children:
    In children, whose heme synthesis is critical for growth and development, an elevated ALA level may signal both toxic exposure (e.g., lead) or rare inherited porphyrias.
  • Adults:
    In adults, high ALA is most often evaluated in the context of occupational or environmental lead exposure.

Generally Normal

  • Standard Levels:
    Low ALA levels are typically considered normal.
  • Clinical Significance:
    There is rarely a clinical condition associated with abnormally low ALA levels, except in scenarios where the entire heme synthesis pathway is suppressed (such as in severe malnutrition or advanced liver failure).

More Info

Related

Liver Function and Metabolic Markers

  • Alanine Aminotransferase of Serum (ALT) & Serum Aspartaminotransferase (AST):
    These enzymes are released when liver cells are damaged. ALT is more liver-specific, while AST is found in various tissues.

  • Gamma Glutamyl Transpeptidase (GGT) & Common Alkaline Phosphatase (ALP):
    Both markers indicate cholestasis and bile duct injury. Elevated levels suggest problems with bile flow that often come with liver dysfunction.

  • Common Blood Bilirubin & Bile Acids:
    These substances provide insight into the liver’s ability to process and excrete waste products. Accumulation can reflect impaired liver function or bile flow obstruction.

  • Serum Ammonia:
    As the liver normally detoxifies ammonia produced during protein metabolism, high serum ammonia levels point to reduced hepatic detoxification capacity.

  • Serum Ceruloplasmin:
    This copper-binding protein, produced by the liver, is a marker for synthetic liver function and disturbances in copper metabolism.

  • Delta‑Aminolevulinic Acid (ALA):
    A precursor in heme synthesis, abnormal ALA levels can reflect disruptions in liver metabolism and may be relevant in conditions like porphyrias.

  • Glutamated Hydrogenase:
    Likely referring to glutamate dehydrogenase, an enzyme involved in amino acid metabolism; its elevation can indicate mitochondrial injury within liver cells.

  • Indican:
    An indirect marker that may rise when the liver’s capacity to process certain metabolic byproducts is impaired.

Together, these markers provide a comprehensive picture of liver health by assessing both hepatocellular integrity and the efficiency of metabolic and excretory processes.

All Markers