Overview and Clinical Significance
Delta-Aminolevulinic Acid (ALA) is a precursor in the heme biosynthesis pathway, playing a crucial role in red blood cell production and mitochondrial function. It is synthesized in the liver and converted into porphobilinogen (PBG), a key intermediate in heme formation.
Clinical Significance
- Heme Synthesis & Anemia: ALA is essential for hemoglobin production, and disruptions in its metabolism can lead to anemia and porphyria.
- Porphyrias & Neurological Effects: Accumulation of ALA is linked to acute hepatic porphyrias, causing neurological symptoms, abdominal pain, and autonomic dysfunction.
- Toxicity & Environmental Exposure: Elevated ALA levels may indicate lead poisoning, as lead inhibits enzymes in the heme pathway.
- Kidney Function & Metabolism: ALA levels are monitored in renal disease, as impaired clearance can lead to accumulation.
ALA is a key biomarker in porphyria diagnostics, toxicology assessments, and metabolic health evaluations.